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Double outlet right ventricle

disorder
SNOMED 7484005CUI C0013069

Overview

Source: MedlinePlus.gov, National Library of Medicine. Not a substitute for medical advice.

Research Evidence

Peer-reviewed studies linked via MeSH term "Double Outlet Right Ventricle" from the MEDLINE/PubMed database.

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Double-chambered Left Ventricle: Clinical Features Comparison between Children and Adults.
[object Object] · J Coll Physicians Surg Pak · 2019
PMID: 31659968Meta-Analysis
Congenital Conundrum: Unraveling the Puzzle of Double Outlet Right Ventricle for the Neonatologist.
[object Object], [object Object], [object Object] et al. · Neoreviews · 2025
PMID: 40588272Review
Single and Double Root Translocation for Transposition and Malposition of the Great Arteries.
[object Object], [object Object], [object Object] · Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu · 2025
PMID: 40382126Review
Recent advances in multimodal imaging in tetralogy of fallot and double outlet right ventricle.
[object Object], [object Object], [object Object] et al. · Curr Opin Cardiol · 2024
PMID: 38652290Review
Double outlet right ventricle - the 50% rule has always been about the conus.
[object Object], [object Object] · Curr Opin Cardiol · 2024
PMID: 38391276Review
Congenital Heart Disease Illustrated: Use of Cross-sectional Imaging in Pediatric Cardiology.
[object Object], [object Object], [object Object] et al. · J Thorac Imaging · 2024
PMID: 37199404Review
Molecular Pathways and Animal Models of Tetralogy of Fallot and Double Outlet Right Ventricle.
[object Object] · Adv Exp Med Biol · 2024
PMID: 38884739Review
Clinical Presentation and Therapy of Tetralogy of Fallot and Double-Outlet Right Ventricle.
[object Object], [object Object], [object Object] · Adv Exp Med Biol · 2024
PMID: 38884737Review
En Bloc Rotation of the Outflow Tracts - Double Root Translocation.
[object Object], [object Object], [object Object] · Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu · 2024
PMID: 38522875Review
Human Genetics of Tetralogy of Fallot and Double-Outlet Right Ventricle.
[object Object], [object Object], [object Object] et al. · Adv Exp Med Biol · 2024
PMID: 38884738Review

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Double-outlet right ventricle
Always present (100%)HP:0001719
Blue discoloration of the skin
Very frequent (80-99%)HP:0000961
Abnormal external ear cartilage morphology
Frequent (30-79%)HP:3000022
Cardiac murmur
Frequent (30-79%)HP:0030148
Cleft of palate
Frequent (30-79%)HP:0000175
Decreased body height
Frequent (30-79%)HP:0004322
Depressed nasal root/bridge
Frequent (30-79%)HP:0005280
Feeding difficulties
Frequent (30-79%)HP:0011968
Hypoplastic left heart
Frequent (30-79%)HP:0004383
Increased distance between eyes
Frequent (30-79%)HP:0000316
Mental retardation, mild
Frequent (30-79%)HP:0001256
Narrow eyelid opening
Frequent (30-79%)HP:0045025
Narrow mouth
Frequent (30-79%)HP:0000160
Pulmonary stenosis
Frequent (30-79%)HP:0001642
Racing heart
Frequent (30-79%)HP:0001649
Submucous cleft hard palate
Frequent (30-79%)HP:0000176
Tachypnea
Frequent (30-79%)HP:0002789
Undergrowth
Frequent (30-79%)HP:0001508
VSD
Frequent (30-79%)HP:0001629
Absent/underdeveloped thymus
Occasional (5-29%)HP:0010515
Atresia of the pulmonary artery
Occasional (5-29%)HP:0004935
Heterotaxia
Occasional (5-29%)HP:0030853
Hypoparathyroidism
Occasional (5-29%)HP:0000829
Intestinal malrotation
Occasional (5-29%)HP:0002566
Low blood calcium levels
Occasional (5-29%)HP:0002901
Tetrology of fallot
Occasional (5-29%)HP:0001636
Truncus arteriosus
Occasional (5-29%)HP:0001660
Aortic coarctation
HP:0001680
Broad big toe
HP:0010055
Common atrioventricular canal
HP:0001674

Quick Facts

SNOMED CT
7484005
UMLS CUI
C0013069
Fully Specified Name
Double outlet right ventricle (disorder)
Specialists
0
Diagnostic Biomarkers
0
HPO Phenotypes
30
Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.