Familial idiopathic pulmonary fibrosis

disorder

SNOMED 426437004CUI C4721952

Overview

Source: MedlinePlus.gov, National Library of Medicine. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Clubbing of fingers

Frequent (30-79%)HP:0100759

Pulmonary fibrosis

Frequent (30-79%)HP:0002206

Alveolar cell carcinoma

HP:0006519

Cirrhosis

HP:0001394

Coughing

HP:0012735

Decreased DLCO

HP:0045051

Elevated bronchoalveolar lavage fluid neutrophil proportion

HP:0032977

Exertional dyspnea

HP:0002875

Hypergammaglobulinaemia

HP:0010702

Panting

HP:0002094

Pulmonary artery hypertension

HP:0002092

Usual interstitial pneumonia

HP:0031950

Related Conditions

Familial disease(parent)

Lung consolidation(parent)

Inflammatory disorder of lower respiratory tract(parent)

Inflammation of specific body organs(parent)

Idiopathic disease(parent)

Fibrosis of lung(parent)

Chronic interstitial lung disease(parent)

Quick Facts

SNOMED CT: 426437004
UMLS CUI: C4721952
Fully Specified Name: Familial idiopathic pulmonary fibrosis (disorder)
Specialists: 0
Diagnostic Biomarkers: 0
HPO Phenotypes: 12

Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.