Heritable pulmonary arterial hypertension

disorder

SNOMED 697897003CUI C0340543

Overview

Source: MedlinePlus.gov, National Library of Medicine. Not a substitute for medical advice.

Clinical Trials

Total Trials

Recruiting

With Results

Recent Trials

Sotatercept in Pulmonary Arterial Hypertension

NCT07140484Phase 4Recruiting27 enrolled

129 Xenon MRI as a Biomarker for Diagnosis and Response to Therapy in Pulmonary Arterial Hypertension (PAH)

NCT06104228Phase 2Recruiting20 enrolled

Fetal Endoscopic Tracheal Occlusion for Congenital Diaphragmatic Hernia (FETO)

NCT03138863N/ARecruiting10 enrolled

A Study Evaluating the Efficacy and Safety of Ralinepag to Improve Treatment Outcomes in PAH Patients

NCT03626688Phase 3Completed728 enrolled

Characterization of LV Strain Patterns in Mildly Elevated PCWP and PAH.

NCT01800292Phase 4Completed9 enrolled

View all 6 trials on ClinicalTrials.gov

Research Evidence

Peer-reviewed studies linked via MeSH term "Familial Primary Pulmonary Hypertension" from the MEDLINE/PubMed database.

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The prevalence of pathogenic variants in the BMPR2 gene in patients with the idiopathic pulmonary arterial hypertension in the Russian population: sequencing data and meta-analysis.

[object Object], [object Object], [object Object] et al. · Respir Res · 2025

PMID: 40229839Meta-AnalysisFull text (PMC)

Allele-specific control of rodent and human lncRNA KMT2E-AS1 promotes hypoxic endothelial pathology in pulmonary hypertension.

[object Object], [object Object], [object Object] et al. · Sci Transl Med · 2024

PMID: 38198571Meta-AnalysisFull text (PMC)

A Systematic Review of Novel Therapies of Pulmonary Arterial Hypertension.

[object Object], [object Object], [object Object] et al. · Am J Cardiovasc Drugs · 2024

PMID: 37945977Meta-AnalysisFull text (PMC)

Heterogeneity of treatment effects by risk in pulmonary arterial hypertension.

[object Object], [object Object], [object Object] et al. · Eur Respir J · 2023

PMID: 37169384Meta-AnalysisFull text (PMC)

Efficacy and safety of non-prostanoid prostacyclin receptor agonist for pulmonary hypertension: A meta-analysis.

[object Object], [object Object], [object Object] et al. · Pulm Pharmacol Ther · 2023

PMID: 36460268Meta-Analysis

Adherence and Discontinuation of Disease-Specific Therapies for Pulmonary Arterial Hypertension: A Systematic Review and Meta-Analysis.

[object Object], [object Object], [object Object] et al. · Am J Cardiovasc Drugs · 2023

PMID: 36434365Meta-Analysis

The Role of Aryl Hydrocarbon Receptor in the Endothelium: A Systematic Review.

[object Object], [object Object], [object Object] et al. · Int J Mol Sci · 2023

PMID: 37686342Meta-AnalysisFull text (PMC)

Is low-risk status a surrogate outcome in pulmonary arterial hypertension? An analysis of three randomised trials.

[object Object], [object Object], [object Object] et al. · Lancet Respir Med · 2023

PMID: 37230098Meta-AnalysisFull text (PMC)

Minimal Clinically Important Difference in the 6-minute-walk Distance for Patients with Pulmonary Arterial Hypertension.

[object Object], [object Object], [object Object] et al. · Am J Respir Crit Care Med · 2023

PMID: 36629737Meta-AnalysisFull text (PMC)

Pulmonary vasodilator therapies in pulmonary arterial hypertension associated with CHD: a systematic review and network meta-analysis.

[object Object], [object Object], [object Object] et al. · Cardiol Young · 2023

PMID: 36721907Meta-Analysis

Search all PubMed articles for Heritable pulmonary arterial hypertension

Research data from MEDLINE/PubMed

Related Conditions

Familial primary pulmonary hypertension(child)

Sporadic primary pulmonary hypertension(child)

Heritable pulmonary arterial hypertension due to BMPR2 mutation(child)

Heritable pulmonary arterial hypertension due to ALK1 or endoglin mutation(child)

Braddock syndrome(child)

Pulmonary hypertensive arterial disease(parent)

Quick Facts

SNOMED CT: 697897003
UMLS CUI: C0340543
Fully Specified Name: Heritable pulmonary arterial hypertension (disorder)
Specialists: 0
Diagnostic Biomarkers: 0
Clinical Trials: 6

Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.