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IAA - Interrupted aortic arch

disorder
SNOMED 218728005CUI C0152419

Overview

Source: MedlinePlus.gov, National Library of Medicine. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Absent pulse
Very frequent (80-99%)HP:0032554
Cardiac murmur
Very frequent (80-99%)HP:0030148
Left ventricular outflow tract obstruction
Very frequent (80-99%)HP:0032092
Blood pressure substantially higher in upper than lower extremities
Frequent (30-79%)HP:0020142
Blue discoloration of the skin
Frequent (30-79%)HP:0000961
Cardiac anomaly
Frequent (30-79%)HP:0001627
Chronic heart failure
Frequent (30-79%)HP:0001635
Feeding difficulties in infancy
Frequent (30-79%)HP:0008872
High blood pressure
Frequent (30-79%)HP:0000822
Laboured breathing
Frequent (30-79%)HP:0002098
Left ventricular wall hypertrophy
Frequent (30-79%)HP:0001712
Leg edema
Frequent (30-79%)HP:0010741
Postexertional malaise
Frequent (30-79%)HP:0030973
Shock
Frequent (30-79%)HP:0031273
Systolic heart murmur
Frequent (30-79%)HP:0031664
Tachypnea
Frequent (30-79%)HP:0002789
VSD
Frequent (30-79%)HP:0001629
Abnormal ascending aorta morphology
Occasional (5-29%)HP:0031784
Aortic valve regurgitation
Occasional (5-29%)HP:0001659
Aortopulmonary window
Occasional (5-29%)HP:0011604
Bicuspid aortic valve
Occasional (5-29%)HP:0001647
Exertional dyspnea
Occasional (5-29%)HP:0002875
Headache
Occasional (5-29%)HP:0002315
Increased distance between eyes
Occasional (5-29%)HP:0000316
Intermittent claudication
Occasional (5-29%)HP:0004417
PDA
Occasional (5-29%)HP:0001643
Right bundle-branch block
Occasional (5-29%)HP:0011712
Tricuspid regurgitation
Occasional (5-29%)HP:0005180
Truncus arteriosus
Occasional (5-29%)HP:0001660
Aortic valve atresia
Very rare (1-4%)HP:0010883

Quick Facts

SNOMED CT
218728005
UMLS CUI
C0152419
Fully Specified Name
Interrupted aortic arch (disorder)
Specialists
0
Diagnostic Biomarkers
0
HPO Phenotypes
30
Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.