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Isolated right ventricular hypoplasia

disorder
SNOMED 718135001CUI C1848587

Overview

Isolated right ventricular hypoplasia is a disorder.

Auto-generated from clinical reference data. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Blue discoloration of the skin
Very frequent (80-99%)HP:0000961
Hypoxemia
Very frequent (80-99%)HP:0012418
Panting
Very frequent (80-99%)HP:0002094
Right-to-left shunt
Very frequent (80-99%)HP:0001694
Atria septal defect
Frequent (30-79%)HP:0001631
Digital clubbing
Frequent (30-79%)HP:0001217
Dilated right atrium
Frequent (30-79%)HP:0030718
PFO
Frequent (30-79%)HP:0001655
Right-sided heart failure
Frequent (30-79%)HP:0001708
Systolic heart murmur
Frequent (30-79%)HP:0031664
Tiredness
Frequent (30-79%)HP:0012378
Tricuspid regurgitation
Frequent (30-79%)HP:0005180
Abnormal atrioventricular conduction
Occasional (5-29%)HP:0005150
Bidirectional shunt
Occasional (5-29%)HP:0012383
Chronic heart failure
Occasional (5-29%)HP:0001635
Increased heart size
Occasional (5-29%)HP:0001640
Muscular ventricular septal defect
Occasional (5-29%)HP:0011623
Pedal oedema
Occasional (5-29%)HP:0010741
Right bundle-branch block
Occasional (5-29%)HP:0011712
Underdeveloped right heart chamber
HP:0004762

Quick Facts

SNOMED CT
718135001
UMLS CUI
C1848587
Fully Specified Name
Isolated right ventricular hypoplasia (disorder)
Specialists
0
Diagnostic Biomarkers
0
HPO Phenotypes
20
Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.