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Miller Dieker syndrome

disorder
SNOMED 253148005CUI C0265219

Overview

Source: MedlinePlus.gov, National Library of Medicine. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Full upper lip
Always present (100%)HP:0000215
Low intelligence
Always present (100%)HP:0001249
No development of motor milestones
Always present (100%)HP:0001270
Abnormal upper lip morphology
Very frequent (80-99%)HP:0000177
Cerebral cortex atrophy
Very frequent (80-99%)HP:0002120
Decreased projection of mandible
Very frequent (80-99%)HP:0000347
Electroencephalogram abnormal
Very frequent (80-99%)HP:0002353
Fewer or absent grooves in brain
Very frequent (80-99%)HP:0001339
Frontal protuberance
Very frequent (80-99%)HP:0002007
Growth deficiency
Very frequent (80-99%)HP:0001510
High forehead
Very frequent (80-99%)HP:0000348
Increased width of bridge of nose
Very frequent (80-99%)HP:0000431
Nasal hypoplasia
Very frequent (80-99%)HP:0003196
Palpebronasal fold
Very frequent (80-99%)HP:0000286
Posteriorly angulated ears
Very frequent (80-99%)HP:0000358
Abnormality of the cardiovascular system
Frequent (30-79%)HP:0001626
Decreased size of cranium
Frequent (30-79%)HP:0000252
Deep palmar creases
Frequent (30-79%)HP:0006191
Hydramnios
Frequent (30-79%)HP:0001561
Large cavum septi pellucidi
Frequent (30-79%)HP:0002389
Low-set ears
Frequent (30-79%)HP:0000369
Midline brain calcifications
Frequent (30-79%)HP:0007045
Small for gestational age infant
Frequent (30-79%)HP:0001511
Abnormality of cardiovascular system morphology
Occasional (5-29%)HP:0030680
Ataxia
Occasional (5-29%)HP:0001251
Contractures of the hands
Occasional (5-29%)HP:0009473
Curvature of little finger
Occasional (5-29%)HP:0004209
Hypoplasia of corpus callosum
Occasional (5-29%)HP:0002079
Kidney disease
Occasional (5-29%)HP:0000112
Sacral dimple
Occasional (5-29%)HP:0000960

Quick Facts

SNOMED CT
253148005
UMLS CUI
C0265219
Fully Specified Name
Miller Dieker syndrome (disorder)
Specialists
0
Diagnostic Biomarkers
0
HPO Phenotypes
30
Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.