Overview
Selective IgM immunodeficiency is a disorder.
Auto-generated from clinical reference data. Not a substitute for medical advice.
Signs & Symptoms
Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.
Decreased circulating total IgM
Very frequent (80-99%)HP:0002850
Predisposition to infections
Very frequent (80-99%)HP:0002719
respiratory infections, recurrent
Very frequent (80-99%)HP:0002205
Unusual course of infection
Very frequent (80-99%)HP:0032169
Allergy
Frequent (30-79%)HP:0012393
Autoimmunity
Frequent (30-79%)HP:0002960
Decreased specific antibody response to vaccination
Frequent (30-79%)HP:0032140
Pulmonary infections
Frequent (30-79%)HP:0006532
Recurrent sinus infections
Frequent (30-79%)HP:0011108
Recurrent URI
Frequent (30-79%)HP:0002788
Antinuclear antibodies
Occasional (5-29%)HP:0003493
Bacterial infection of skin
Occasional (5-29%)HP:0100658
Bronchiectasis
Occasional (5-29%)HP:0002110
Bronchitis, recurrent
Occasional (5-29%)HP:0002837
Chronic diarrhoea
Occasional (5-29%)HP:0002028
Chronic extreme exhaustion
Occasional (5-29%)HP:0012432
Chronic oral thrush
Occasional (5-29%)HP:0009098
Chronic sinus disease
Occasional (5-29%)HP:0011109
Corneal inflammation
Occasional (5-29%)HP:0000491
Decreased proportion of CD19+CD38+IgM+ cells
Occasional (5-29%)HP:0030380
Decreased proportion of CD4-positive T cells
Occasional (5-29%)HP:0032218
Growth deficiency
Occasional (5-29%)HP:0001510
Immune thrombocytopenia
Occasional (5-29%)HP:0001973
Infection in blood stream
Occasional (5-29%)HP:0100806
Meningitis
Occasional (5-29%)HP:0001287
Nasal allergies
Occasional (5-29%)HP:0003193
Neurodermatitis
Occasional (5-29%)HP:0001047
Neutropenia in presence of anti-neutropil antibodies
Occasional (5-29%)HP:0001904
Non-infectious meningitis
Occasional (5-29%)HP:0033430
Nontuberculous mycobacterial pulmonary infection
Occasional (5-29%)HP:0032261
Related Conditions
Quick Facts
- SNOMED CT
- 190980000
- UMLS CUI
- C0154275
- Fully Specified Name
- Selective immunoglobulin M deficiency (disorder)
- Specialists
- 0
- Diagnostic Biomarkers
- 0
- HPO Phenotypes
- 30
Medical Disclaimer
This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.
Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.