← Back to Conditions

Spondyloepiphyseal dysplasia Maroteaux type

disorder
SNOMED 719204007CUI C3159322

Overview

Spondyloepiphyseal dysplasia Maroteaux type is a disorder.

Auto-generated from clinical reference data. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Decreased body height
Always present (100%)HP:0004322
Flattened vertebral bodies
Always present (100%)HP:0000926
Generalized osteoporosis with pathologic fractures
Always present (100%)HP:0040160
Genu valga
Always present (100%)HP:0002857
Hypoplastic femoral neck
Always present (100%)HP:0100864
Short hands
Always present (100%)HP:0004279
Spondyloepiphyseal dysplasia
Always present (100%)HP:0002655
Short neck
Frequent (30-79%)HP:0000470
Atlantoaxial instability
Occasional (5-29%)HP:0003467
Broad chest
Occasional (5-29%)HP:0000914
Fallen arches
Occasional (5-29%)HP:0001763
Kyphoscoliosis
Occasional (5-29%)HP:0002751
Pectus carinatum
Occasional (5-29%)HP:0000768
Small joint hypermobilty
Occasional (5-29%)HP:0430046
Cloudy cornea
Excluded (<1%)HP:0007759
Low intelligence
Excluded (<1%)HP:0001249
Mucopolysacchariduria
Excluded (<1%)HP:0008155

Quick Facts

SNOMED CT
719204007
UMLS CUI
C3159322
Fully Specified Name
Spondyloepiphyseal dysplasia Maroteaux type (disorder)
Specialists
0
Diagnostic Biomarkers
0
HPO Phenotypes
17
Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.